Autoimmune lymphoproliferative syndrome (ALPS): a rare cause of immune cytopenia.
نویسندگان
چکیده
Autoimmune Lymphoproliferative syndrome (ALPS) is an inherited disorder manifesting with autoimmune cytopenia, lymphadenopathy and splenomegaly. The differential diagnosis includes infections, autoimmune disorders or malignancies. The disease is characterized by accumulation of double negative (CD3+ CD4- CD8-) T cells (DNT) in the peripheral blood. We describe a case and review the literature.
منابع مشابه
Autoimmune Lymphoproliferative Syndrome Misdiagnosed as Hemophagocytic Lymphohistiocytosis A Case Report
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ورودعنوان ژورنال:
- Indian pediatrics
دوره 45 2 شماره
صفحات -
تاریخ انتشار 2008